Choledochal cysts

From Wikipedia, the free encyclopedia

Choledochal cysts
Classification and external resources
ICD-10	Q44.4
ICD-9	751.69
DiseasesDB	2527
eMedicine	article/172099 article/366004 article/934267
MeSH	D015529

Choledochal cysts are congenital conditions associated with benign cystic dilatation of bile ducts. They are uncommon in western countries^[1] but not as rare in East Asian nations like Japan and China.

Contents 1 Presentation 2 Clinical Findings 3 Types 4 Treatments 5 References

[edit] Presentation

Most of them present in 1st year of life; adult presentation is rare and usually at this stage is associated with complication . Classic triad of intermittent abdominal pain, jaundice, and a right upper quadrant abdominal mass is found only in minority of patients.

[edit] Clinical Findings

-Direct Hyperbilirubinemia

[edit] Types

They were classified into 5 types by Todani in 1977^[2].

Classification was based on site of the cyst or dilatation. Type I to IV has been subtyped.

• Type I: Most common variety involving sacular or fusiform dilatation of a portion or entire common bile duct (CBD) with normal intrahepatic duct.
• Type II: Isolated diverticulum protruding from the CBD.
• Type III or Choledochocele: Arise from dilatation of duodenal portion of CBD or where pancreatic duct meets.
• Type IV: Dilatation of both intrahepatic and extrahepatic biliary duct.
• Type V or Caroli's disease: Cystic dilatation of intra hepatic biliary ducts.

[edit] Treatments

Choledochal cysts are treated by surgical excision of the cyst with the formation of a roux-en-Y anastamosis to the biliary duct. Future complications include cholangitis and a 2% risk of malignancy, which may develop in any part of the biliary tree.

[edit] References

1. ^ Liu YB, Wang JW, Devkota KR, et al. (2007). "Congenital choledochal cysts in adults: twenty-five-year experience". Chin. Med. J. 120 (16): 1404–7. PMID 17825168. 
2. ^ Todani T, Watanabe Y, Narusue M, Tabuchi K, Okajima K (1977). "Congenital bile duct cysts: Classification, operative procedures, and review of thirty-seven cases including cancer arising from choledochal cyst". Am. J. Surg. 134 (2): 263–9. doi:10.1016/0002-9610(77)90359-2. PMID 889044. 

v • d • e Health science - Medicine - Cystic diseases Respiratory system Langerhans cell histiocytosis  · Lymphangiomyomatosis · Cystic bronchiectasis Skin Adenoid cystic carcinoma Musculoskeletal system Cystic hygroma · Fibrocystic breast diseaese Digestive system Polycystic Liver Disease · Congenital hepatic fibrosis · Biliary hamartomas · Caroli disease · Choledochal cysts · Von Meyenburg complexes · Peliosis hepatis Nervous system Cystic leukoencephalopathy Genitourinary system Polycystic kidney disease (Autosomal dominant polycystic kidney, Autosomal recessive polycystic kidney)  · Medullary cystic kidney disease (Nephronophthisis)  · Congenital cystic dysplasia Other conditions Hydatid cyst · Von Hippel-Lindau syndrome · Tuberous sclerosis

v • d • e Congenital malformations and deformations of digestive system (Q35-Q45, 749-751) Upper GI tract Tongue, mouth and pharynx Cleft lip and palate · Van der Woude syndrome · tongue (Ankyloglossia, Macroglossia, Hypoglossia) Esophagus EA/TEF (Esophageal atresia: types A, B, C, and D, Tracheoesophageal fistula: types B, C, D and E) esophageal rings (Esophageal web  · upper, Schatzki ring · lower) Stomach Pyloric stenosis · Hiatus hernia Lower GI tract Intestines Intestinal atresia (Duodenal atresia) · Meckel's diverticulum · Hirschsprung's disease · Intestinal malrotation · Dolichocolon · Enteric duplication cyst Rectum/anus Imperforate anus · Persistent cloaca Accessory Pancreas Annular pancreas · Accessory pancreas · Johanson-Blizzard syndrome Pancreas divisum Bile duct Choledochal cysts (Caroli disease) · Biliary atresia Liver Alagille syndrome mouth navs: anat/dev, noncongen/congen face/congen GI/neoplasia, symptoms, proc digestive system navs: anat of tract,glands,perit,diaphragm/physio/dev, noncongen/congen/congen of d+w/neoplasia, symptoms+signs/eponymous, proc

This medical article is a stub. You can help Wikipedia by expanding it. v • d • e