Ramsay Hunt syndrome
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(Redirected from Early-onset cerebellar ataxia with myoclonus)
At least three separate neurological syndromes carry the name of Ramsay Hunt syndrome (RHS), their only connection being that they were all first described by James Ramsay Hunt (1872–1937):
- Ramsay Hunt syndrome type I, also called Ramsay Hunt cerebellar syndrome, is a rare form of cerebellar degeneration which involves myoclonic epilepsy, progressive ataxia, tremor, and a dementing process.
- Ramsay Hunt syndrome type II is the reactivation syndrome of herpes zoster in the geniculate ganglion. It has variable presentation which may include a lower motor neuron lesion of the facial nerve, deafness, vertigo, and pain.
- Ramsay Hunt syndrome type III is a less commonly referenced condition, an occupationally induced neuropathy of the deep palmar branch of the ulnar nerve. It is also called Hunt's disease or Artisan's palsy.
- "Ramsay Hunt Syndrome". Retrieved 2011-05-12.
- "NINDS Dyssynergia Cerebellaris Myoclonica Information Page". National Institute of Neurological Disorders and Stroke. 14 February 2011. Retrieved 6 January 2015.
- Hunt JR (1907). "On herpetic inflammations of the geniculate ganglion: a new syndrome and its complications". J Nerv Ment Dis 34 (2): 73–96. doi:10.1097/00005053-190702000-00001.
- Sweeney CJ, Gilden DH (August 2001). "Ramsay Hunt Syndrome". J. Neurol. Neurosurg. Psychiatr. 71 (2): 149–54. doi:10.1136/jnnp.71.2.149. PMC 1737523. PMID 11459884.
- http://www.ramsayhunt.org/epon.shtml Ramsay Hunt Syndrome