Hypoplastic right heart syndrome

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Hypoplastic right heart syndrome
Classification and external resources
ICD-10 Q22.6
ICD-9 746.8 (CDC/BPA 746.882)

Hypoplastic right heart syndrome is a condition where the right atrium and right ventricle are underdeveloped.

It is less common than hypoplastic left heart syndrome.

In some cases it can be identified prenatally.[1]

It can be associated with aortic stenosis.[2]


  1. ^ Paulick J, Tennstedt C, Schwabe M, Körner H, Bommer C, Chaoui R (May 2004). "Prenatal diagnosis of an isochromosome 5p in a fetus with increased nuchal translucency thickness and pulmonary atresia with hypoplastic right heart at 14 weeks". Prenat. Diagn. 24 (5): 371–4. doi:10.1002/pd.877. PMID 15164412. 
  2. ^ Sharma J, Friedman D, Schiller M, Flynn P, Alonso ML (December 1997). "Aortic stenosis in hypoplastic right heart syndrome, associated with interstitial deletion of chromosome 2". Int. J. Cardiol. 62 (3): 199–202. doi:10.1016/S0167-5273(97)00255-6. PMID 9476678.