Polysplenia is a congenital disease manifested by multiple small accessory spleens.
There are frequent associated congenital anomalies all related to deviations in the development of anatomical asymmetries in early embryonic stages. These conditions considered together are called "polysplenia syndrome".
Associated conditions include heterotaxy syndrome, intestinal malrotation, situs inversus, biliary atresia, and the range of congenital cardiac malformations most commonly dextrocardia, atrial situs ambiguus, ventricular inversion, and VA concordance with left posterior aorta.
Although present, the multiple small spleens are ineffective; this is termed functional asplenia.
anat (h, u, t, a, l)/phys/devp