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Ubiquinol-cytochrome c reductase hinge protein
Protein UQCRH PDB 1bcc.png
PDB rendering based on 1bcc.
Available structures
PDB Ortholog search: PDBe, RCSB
Symbols UQCRH ; QCR6; UQCR8
External IDs OMIM613844 MGI1913826 HomoloGene103848 GeneCards: UQCRH Gene
EC number
Species Human Mouse
Entrez 7388 66576
Ensembl ENSG00000173660 ENSMUSG00000063882
UniProt P07919 P99028
RefSeq (mRNA) NM_006004 NM_025641
RefSeq (protein) NP_005995 NP_079917
Location (UCSC) Chr 1:
46.77 – 46.78 Mb
Chr 4:
116.07 – 116.08 Mb
PubMed search [1] [2]

Cytochrome b-c1 complex subunit 6, mitochondrial is a protein that in humans is encoded by the UQCRH gene.[1][2]

Its gene product is a subunit of the respiratory chain protein Ubiquinol Cytochrome c Reductase (UQCR, Complex III or Cytochrome bc1 complex; E.C., which consists of the products of one mitochondrially encoded gene, MTCYTB (mitochondrial cytochrome b) and ten nuclear genes: UQCRC1, UQCRC2, Cytochrome c1, UQCRFS1 (Rieske protein), UQCRB, "11kDa protein", UQCRH (cyt c1 Hinge protein), Rieske Protein presequence, "cyt. c1 associated protein", and "Rieske-associated protein".


  1. ^ Ohta S, Goto K, Arai H, Kagawa Y (Jan 1988). "An extremely acidic amino-terminal presequence of the precursor for the human mitochondrial hinge protein". FEBS Lett 226 (1): 171–5. doi:10.1016/0014-5793(87)80573-2. PMID 2826252. 
  2. ^ "Entrez Gene: UQCRH ubiquinol-cytochrome c reductase hinge protein". 

Further reading[edit]