Congenital self-healing reticulohistiocytosis

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Congenital self-healing reticulohistiocytosis (also known as "Hashimoto–Pritzker disease,"[1] and "Hashimoto–Pritzker syndrome"[2]) is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]:720


Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]

See also[edit]


  1. ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0. 
  2. ^ a b James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0. 
  3. ^ "Langerhans Cell Histiocytosis - Patient UK". Retrieved 2007-05-10.