3D model (JSmol)
|Molar mass||222.26 g·mol−1|
Except where otherwise noted, data are given for materials in their standard state (at 25 °C [77 °F], 100 kPa).
|what is ?)(|
Cystathionine is an intermediate in the synthesis of cysteine.
Cystathionine is produced by the transsulfuration pathway which converts homocysteine into cystathionine. The cystathionine is then used by the cystathionine gamma-lyase CTH, cysteine dioxygenase CDO, and cysteine sulfinic acid decarboxylase CSAD gene enzymes to produce hypotaurine and then taurine.
An excess of cystathionine in the urine is called cystathioninuria.
Biosynthetically, cystathionine is generated from homocysteine and serine by cystathionine beta synthase (upper reaction in the diagram below). It is then cleaved into cysteine and α-ketobutyrate by cystathionine gamma-lyase (lower reaction).
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