Cystathionine

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Cystathionine
Skeletal formula of cystathionine
Ball-and-stick model of the cystathionine molecule as a zwitterion
Names
IUPAC name
2-amino-4-(2-amino-2-carboxy-ethyl) thio-butanoic acid
Other names
L-Cystathionine; S-[(2R)-2-Amino-2-carboxyethyl]-L-homocysteine
Identifiers
56-88-2 YesY
ChEBI CHEBI:17755 YesY
ChEMBL ChEMBL209241 YesY
ChemSpider 811 YesY
Jmol-3D images Image
KEGG C00542 YesY
MeSH Cystathionine
PubChem 834
Properties
C7H14N2O4S
Molar mass 222.263 g/mol
Except where otherwise noted, data are given for materials in their standard state (at 25 °C [77 °F], 100 kPa).
 YesY verify (what isYesY/N?)
Infobox references

Cystathionine is an intermediate in the synthesis of cysteine.

It is generated from homocysteine and serine by cystathionine beta synthase.

It is cleaved into cysteine and α-ketobutyrate by cystathionine gamma-lyase.

An excess in the urine is called cystathioninuria.

Cysteine metabolism. Cystathionine beta synthase catalyzes the upper reaction and cystathionine gamma-lyase catalyzes the lower reaction.