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  • Thumbnail for Medium-chain acyl-coenzyme A dehydrogenase deficiency
    Medium-chain acyl-CoA dehydrogenase deficiency (MCAD deficiency or MCADD) is a disorder of fatty acid oxidation that impairs the body's ability to break...
    15 KB (1,670 words) - 22:40, 29 December 2023
  • specificity for short-, medium-, or long-chain fatty acid acyl-CoA substrates. While different dehydrogenases target fatty acids of varying chain length, all types...
    17 KB (2,171 words) - 04:03, 25 March 2024
  • Thumbnail for Medium-chain acyl-CoA dehydrogenase
    Medium-chain acyl-CoA dehydrogenase (EC 1.3.8.7, fatty acyl coenzyme A dehydrogenase (ambiguous), acyl coenzyme A dehydrogenase (ambiguous), acyl dehydrogenase...
    5 KB (558 words) - 23:43, 29 March 2024
  • Thumbnail for ACADM
    tissue. Medium-chain fatty acids are also produced when larger fatty acids are degraded. The acyl-coenzyme A dehydrogenase for medium-chain fatty acids...
    7 KB (955 words) - 09:28, 29 January 2023
  • Avoiding infant formulas with medium-chain triglycerides as the main fat source Long-chain hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency is a mitochondrial...
    32 KB (3,362 words) - 15:08, 28 May 2024
  • Thumbnail for Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
    Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting...
    5 KB (399 words) - 20:41, 30 May 2024
  • Thumbnail for Short-chain acyl-CoA dehydrogenase
    Short-chain acyl-CoA dehydrogenase (EC 1.3.8.1, butyryl-CoA dehydrogenase, butanoyl-CoA dehydrogenase, butyryl dehydrogenase, unsaturated acyl-CoA reductase...
    4 KB (431 words) - 03:14, 30 March 2024
  • and short chain fatty acids; for this reason this disorder is sometimes called medium- and short-chain 3-hydroxyacyl-coenzyme A dehydrogenase (M/SCHAD)...
    4 KB (410 words) - 00:38, 2 August 2020
  • Thumbnail for Sorbitol dehydrogenase
    evolutionary relationship with alcohol dehydrogenase, which also belongs to the protein superfamily of medium-chain dehydrogenase/reductase enzymes (MDRs). Mammalian...
    7 KB (896 words) - 07:30, 3 June 2024
  • Thumbnail for Glycerol-3-phosphate dehydrogenase
    electron transport chain in the mitochondria. Older terms for glycerol-3-phosphate dehydrogenase include alpha glycerol-3-phosphate dehydrogenase (alphaGPDH)...
    23 KB (2,206 words) - 14:20, 26 August 2023
  • Thumbnail for Alcohol dehydrogenase
    (December 2008). "Medium- and short-chain dehydrogenase/reductase gene and protein families : Dual functions of alcohol dehydrogenase 3: implications with...
    50 KB (5,566 words) - 06:06, 3 June 2024
  • ACADM or MCAD, a gene Medium-chain acyl-CoA dehydrogenase, an enzyme used in lipid metabolism Medium-chain acyl-coenzyme A dehydrogenase deficiency (MCAD deficiency...
    628 bytes (95 words) - 02:27, 24 October 2022
  • Thumbnail for Inborn error of lipid metabolism
    A dehydrogenase deficiency (LCHAD) - Long-chain 3-hydroxyacyl-coenzyme A Medium-chain acyl-coenzyme A dehydrogenase deficiency (MCAD) - Medium-chain acyl-coenzyme...
    4 KB (356 words) - 21:16, 7 December 2020
  • Thumbnail for Long-chain-aldehyde dehydrogenase
    Fatty aldehyde dehydrogenase (or long-chain-aldehyde dehydrogenase) is an aldehyde dehydrogenase enzyme that in human is encoded in the ALDH3A2 gene on...
    5 KB (613 words) - 00:23, 4 April 2024
  • microsomal short-chain dehydrogenase/reductase and cytosolic medium-chain alcohol dehydrogenases. In Bovine, retinol dehydrogenase is found as a part...
    14 KB (1,491 words) - 22:48, 27 March 2024
  • Thumbnail for HADHA
    associated with trifunctional protein deficiency or long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. HADHA is an 82.9 kDa protein composed of...
    12 KB (1,371 words) - 14:19, 16 June 2023
  • Thumbnail for Fatty acid
    2013. ISBN 978-1-118-16945-2. Roth, Karl S. (2013-12-19). "Medium-Chain Acyl-CoA Dehydrogenase Deficiency". Medscape. Beermann, C.; Jelinek, J.; Reinecker...
    54 KB (5,037 words) - 00:57, 30 March 2024
  • fatty acid metabolism Long-chain hydroxyacyl-CoA dehydrogenase deficiency (LCHAD) > 1 in 75,000 Medium-chain acyl-CoA dehydrogenase deficiency (MCAD) > 1 in...
    7 KB (716 words) - 06:19, 9 June 2024
  • Thumbnail for Hydroxyacyl-Coenzyme A dehydrogenase
    3-hydroxyacyl-CoA dehydrogenase gene family. The encoded protein functions in the mitochondrial matrix to catalyze the oxidation of straight-chain 3-hydroxyacyl-CoAs...
    7 KB (959 words) - 02:18, 10 March 2024
  • and severe hypoglycemia. Disorders of fatty acid oxidation Medium chain acylCoA dehydrogenase deficiency (MCAD) Familial Leucine sensitive hypoglycemia...
    21 KB (1,265 words) - 01:46, 22 December 2023
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