Ramsay Hunt syndrome
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(Redirected from Early-onset cerebellar ataxia with myoclonus)
- Ramsay Hunt syndrome type 1, also called Ramsay Hunt cerebellar syndrome, is a rare form of cerebellar degeneration which involves myoclonic epilepsy, progressive ataxia, tremor, and a dementing process.
- Ramsay Hunt syndrome type 2 is the reactivation of herpes zoster in the geniculate ganglion. It is sometimes called herpes zoster oticus, and has variable presentation which may include a lower motor neuron lesion of the facial nerve, deafness, vertigo, and pain. A triad of ipsilateral facial paralysis, ear pain, and vesicles on the face, on the ear, or in the ear is the typical presentation.
- Ramsay Hunt syndrome type 3 is a less commonly referenced condition, an occupationally induced neuropathy of the deep palmar branch of the ulnar nerve. It is also called Hunt's disease or Artisan's palsy.
- "NINDS Dyssynergia Cerebellaris Myoclonica Information Page". National Institute of Neurological Disorders and Stroke. 14 February 2011. Retrieved 6 January 2015.
- Ramsay Hunt, J. (1907). "On herpetic inflammations of the geniculate ganglion: a new syndrome and its complications". Journal of Nervous and Mental Disease. 34 (2): 73–96. doi:10.1097/00005053-190702000-00001.
- Sweeney, C.J.; Gilden, D.H. (August 2001). "Ramsay Hunt Syndrome". Journal of Neurology, Neurosurgery, and Psychiatry. 71 (2): 149–54. doi:10.1136/jnnp.71.2.149. PMC . PMID 11459884.
- Pearce, J.M.S. (2007). "Some Syndromes of James Ramsay Hunt". Practical Neurology. 7 (3): 182–185. PMID 17515597. Retrieved 8 July 2016.