Pagetoid reticulosis

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Pagetoid reticulosis
Classification and external resources
ICD-10 C84.0
ICD-O 9700/3
MeSH D056267
Orphanet 178517

Pagetoid reticulosis (also known as "acral mycoses fungoides",[1] "localized epidermotropic reticulosis",[1] "mycosis fungoides palmaris et plantaris",[1] "unilesional mycosis fungoides",[2] and "Woringer–Kolopp disease"[1]) is a cutaneous condition, an uncommon lymphoproliferative disorder, sometimes considered a form of mycosis fungoides.[1]:734

Symptoms and Signs[edit]

Lesions emerge as well-demarcated psoriasiform or hyperkeratotic patches and 36 plaques,with a central clearing and an elevated border[3]. Pagetoid reticulosis is a very slow progressive variant of mycosis fungoides and is usually localized unlike the latter [4].

Cause[edit]

Diagnosis[edit]

Treatment[edit]

The most common method of treatment includes radiotherapy and/or surgical excision [5].

See also[edit]

References[edit]

  1. ^ a b c d e James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0. 
  2. ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0. 
  3. ^ Harvey, Nathan T.; Spagnolo, Dominic V.; Wood, Benjamin A. (2015-12-01). "‘Could it be mycosis fungoides?’: an approach to diagnosing patch stage mycosis fungoides". Journal of Hematopathology. 8 (4): 209–223. ISSN 1868-9256. doi:10.1007/s12308-015-0247-2. 
  4. ^ Willemze, Rein; Jaffe, Elaine S.; Burg, Günter; Cerroni, Lorenzo; Berti, Emilio; Swerdlow, Steven H.; Ralfkiaer, Elisabeth; Chimenti, Sergio; Diaz-Perez, José L. (2005-05-15). "WHO-EORTC classification for cutaneous lymphomas". Blood. 105 (10): 3768–3785. ISSN 0006-4971. PMID 15692063. doi:10.1182/blood-2004-09-3502. 
  5. ^ Beigi, Pooya Khan Mohammad (2017). Clinician's Guide to Mycosis Fungoides. Springer International Publishing. pp. 35–36. ISBN 9783319479064. doi:10.1007/978-3-319-47907-1_7.