Hemangioendothelioma

Hemangioendothelioma
Classification and external resources
ICD-O:	9130-9133
MeSH	D006390

Hemangioendothelioma is used to describe a group of vascular neoplasms that may be considered benign or malignant in their activity.

Presentation

They have been described as masses that fall between a hemangioma and angiosarcoma. They are vascular tumors that commonly present with an enlarging mass and most commonly involve the lungs, liver, and musculoskeletal system, although many other body sites have been reported, including the head and neck, intestines, lymph nodes, pleura, retroperitoneum, stomach.

Treatment

Treatment is varied and depends on the site and extent of tumor involvement, site(s) of metastasis, and specific individual factors. Surgical resection, radiotherapy, and chemotherapy have all been used to treat these masses, although studies on survival have yet to be conducted to delineate various treatment regimens.

Types of hemangioendotheliomas

• Epithelioid

• Kaposiform

• Retiform

See also

• Infantile hemangioendothelioma

External links

• Hemgioendothelioma Support Group
• Maxillofacialcenter
• H.E.A.R.D. Hemangioendothelioma, Epithelioid Hemangioendothelioma And Related vascular Disorders Support Group and International H.E.A.R.D. Registry