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User:Purplereign1/Ross' syndrome

From Wikipedia, the free encyclopedia

Ross' syndrome consists of Adie's syndrome (myotonic pupils and absent deep tendon reflexes) plus segmental anhidrosis (typically associated with compensatory hyperhidrosis).[1]

It was characterized in 1958[2][3] by A.T. Ross.[4]

By 1992, eighteen cases had been documented.[5]


Signs and Symptoms

Initial manifestations often include an abnormal segmental sweating response (described as hyperhidrosis or anhidrosis in some patients) and a tonic pupil. Other commonly reported symptoms included fatigue, chronic cough, and increased urinary frequency.[6]


Pathophysiology


Diagnosis


Treatment


Prognosis

Ross syndrome is a non life-threatening benign condition but delay in diagnosis can result in slow progression of autonomic symptoms. [7]


Epidemiology

Ross Syndrome is a progressive autonomic dysfunction that can occur in any age, ethnicity, or gender. The average age of diagnosis for Ross syndrome is 36 years and RS has a slight female predominance.



References


  1. ^ Cline, A; Jorizzo, JL (2017). "Does daily folic acid supplementation reduce methotrexate efficacy?". Dermatology Online Journal. 23 (11). doi:10.5070/d32311037244. ISSN 1087-2108.
  2. ^ Dermatology. Otto Braun-Falco (2nd, completely rev. ed ed.). Berlin: Springer. 2000. ISBN 3-540-59452-3. OCLC 45350598. {{cite book}}: |edition= has extra text (help)CS1 maint: others (link)
  3. ^ Yaşar, Şirin; Aslan, Canan; Serdar, Zehra Aşiran; Demirci, Gülşen Tükenmez; Tutkavul, Kemal; Babalik, Dilek (2010). "Ross syndrome: Unilateral hyperhidrosis, Adie's tonic pupils and diffuse areflexia". JDDG: Journal der Deutschen Dermatologischen Gesellschaft. 8 (12): 1004–1006. doi:10.1111/j.1610-0387.2010.07400.x. ISSN 1610-0387.
  4. ^ Ross, Alexander T. (1958-11-01). "Progressive selective sudomotor denervation: A case with coexisting Adie's syndrome". Neurology. 8 (11): 809–809. doi:10.1212/WNL.8.11.809. ISSN 0028-3878. PMID 13590391.
  5. ^ Weller, Michael; Wilhelm, Helmut; Sommer, Norbert; Dichgans, Johannes; Wiethölter, Horst (1992-04-01). "Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature". Journal of Neurology. 239 (4): 231–234. doi:10.1007/BF00839146. ISSN 1432-1459.
  6. ^ Lamotte, Guillaume; Sandroni, Paola; Cutsforth-Gregory, Jeremy K.; Berini, Sarah E.; Benarroch, Eduardo E.; Shouman, Kamal; Mauermann, Michelle L.; Anderson, Jennifer; Low, Phillip A.; Singer, Wolfgang; Coon, Elizabeth A. (2021-10-01). "Clinical presentation and autonomic profile in Ross syndrome". Journal of Neurology. 268 (10): 3852–3860. doi:10.1007/s00415-021-10531-8. ISSN 1432-1459.
  7. ^ "Ross syndrome | DermNet NZ". dermnetnz.org. Retrieved 2021-12-07.